Pulmonary hypertension (pulmonary arterial hypertension) is an increase in pressure in the pulmonary artery system, which may be due to an increase in resistance in the bloodstream of the lungs or a significant increase in pulmonary blood flow.
Primary pulmonary hypertension is the primary persistent increase in pulmonary artery pressure of unknown origin. The disease is based on concentric fibrosis, hypertrophy of the pulmonary artery medial and its branches, as well as multiple arterio-venous anastomoses.
Primary bronchopulmonary amyloidosis is a primary disease characterized by amyloid deposition in the lung parenchyma, vessel walls, respiratory mucosa, pleura, mediastinal lymph nodes.
Lymphangioliomiomatosis (leiomyomatosis) is a pathological process characterized by tumor-like proliferation of smooth muscle fibers along the course of small bronchi, bronchioles, walls of blood and lymphatic vessels of the lungs followed by small-cystic transformation of lung tissue. The disease affects only women aged 18-50 years.
Alveolar microlithiasis of the lung is a disease characterized by the deposition in the alveoli of substances consisting of mineral compounds and proteins. The disease is rare, occurs at any age, but mostly at the age of 20-40 years. Women are more often ill.
Alveolar proteinosis of the lungs is a disease of unknown etiology, characterized by the accumulation of a protein-lipid substance in the alveoli and moderately progressive dyspnea.
Goodpasture syndrome (hemorrhagic pulmonary-kidney syndrome) is a progressive autoimmune disease of the lungs and kidneys, characterized by the formation of antibodies to the basal membranes of capillaries of the glomeruli of the kidneys and alveoli and manifested by a combination of pulmonary and renal hemorrhages.
Hystiocytosis X of the lungs (histiocytic granulomatosis of the lungs) is a disease of the reticulogistiocytic system of unknown etiology, characterized by the proliferation of histiocytes (cells X) and the formation of histiocytic granulomas in the lungs and other organs and tissues.
The clinical symptoms and severity of manifestations of sarcoidosis are very diverse. It is characteristic that most patients can note a completely satisfactory general condition, despite mediastinal lymphadenopathy and a fairly extensive lung injury.
