Brachioradial and radioulnar synostosis: causes, symptoms, diagnosis, treatment

Bronchial sinostosis

Bronchial sinostosis (syndrome Keutel et al., 1970) is a congenital defect due to impaired differentiation of the osteoarticular apparatus of the arm and is characterized by a pronounced shortening of the upper limb, fusion of the humerus and curved radial bones (absence of the elbow joint), underdevelopment or absence of ulnar bone, one to four rays of the hand, a significant underdevelopment of the muscles. The forearm is usually located at an angle from 170 to 110 ° with respect to the shoulder. Deformation is characterized by a variety of clinical signs (due to the lack of one to four beams of the hand). Correction of deformation is possible: they perform multi-stage orthopedic surgery, including lengthening of the brachial bone by the apparatus method, transplantation of the blood supply to the metatarsophalangeal joints, transposition of the latissimus muscle of the back to the position of the biceps brachii of the shoulder, reconstructive operations on the hand.

ICD-10 code

Q87.2 The brachial synostosis.

Radiobulent synostosis

Radiobulent synostosis is a congenital defect caused by a violation of the differentiation of the osteoarticular apparatus of the forearm and characterized by the fusion of the radial and ulnar bones in the proximal part. Often diagnosed dislocation of the head of the radius.

ICD-10 code

Q74.0 Radiostar synostosis.

Symptoms and Diagnosis of the Brachial and Radiobulent Synostosis

Clinical signs of synostosis are usually found from the age of 3 years, when there is a noticeable lack of pronation and supination of the forearm. The forearm is in the position of pronation. Isolate bilateral deformation (with a large length of synostosis and the presence of a common bone marrow channel of the radial and ulnar bones) and one-sided deformation (with a smaller length of fusion).

Subcompensation of this deficiency in children's movements is caused by rotation in the shoulder joint with the elbow joint straightened, as well as by excessive stretching of the tendon-ligament apparatus of the wrist joint. Touching the face is possible with the back surface of the brush.

Treatment of the brachial and radiolar synostosis

Operative treatment is performed in the case of pronounced pronational contracture of the hand (more than 15 ° from the average position of the hand) in order to place the forearm and hand in a functionally advantageous position (15 ° pronation).